β - Hekzosaminidaz a ve sialidaz enzim eksikliği olan farelerde beyin lipid profilinin çıkarılması

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β - Hekzosaminidaz a ve sialidaz enzim eksikliği olan farelerde beyin lipid profilinin çıkarılması

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Tay-Sachs hastalığı
Sialidaz
Fare modeli

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